Guidelines for the use and interpretation of assays for monitoring autophagy (4th edition)1 DJ Klionsky, AK Abdel-Aziz, S Abdelfatah, M Abdellatif, A Abdoli, S Abel, ... autophagy 17 (1), 1-382, 2021 | 10709 | 2021 |
Transgenics, toxicity and therapeutics in rodent models of mutant SOD1-mediated familial ALS BJ Turner, K Talbot Progress in neurobiology 85 (1), 94-134, 2008 | 610 | 2008 |
TDP-43 triggers mitochondrial DNA release via mPTP to activate cGAS/STING in ALS CH Yu, S Davidson, CR Harapas, JB Hilton, MJ Mlodzianoski, ... Cell 183 (3), 636-649. e18, 2020 | 524 | 2020 |
Intercellular propagated misfolding of wild-type Cu/Zn superoxide dismutase occurs via exosome-dependent and-independent mechanisms LI Grad, JJ Yerbury, BJ Turner, WC Guest, E Pokrishevsky, MA O’Neill, ... Proceedings of the National Academy of Sciences 111 (9), 3620-3625, 2014 | 447 | 2014 |
Induction of the unfolded protein response in familial amyotrophic lateral sclerosis and association of protein-disulfide isomerase with superoxide dismutase 1 JD Atkin, MA Farg, BJ Turner, D Tomas, JA Lysaght, J Nunan, A Rembach, ... Journal of Biological Chemistry 281 (40), 30152-30165, 2006 | 353 | 2006 |
Emerging therapies and challenges in spinal muscular atrophy MA Farrar, SB Park, S Vucic, KA Carey, BJ Turner, TH Gillingwater, ... Annals of neurology 81 (3), 355-368, 2017 | 250 | 2017 |
Impaired extracellular secretion of mutant superoxide dismutase 1 associates with neurotoxicity in familial amyotrophic lateral sclerosis BJ Turner, JD Atkin, MA Farg, A Rembach, EC Lopes, JD Patch, AF Hill, ... Journal of Neuroscience 25 (1), 108-117, 2005 | 228 | 2005 |
The bone morphogenetic protein axis is a positive regulator of skeletal muscle mass CE Winbanks, JL Chen, H Qian, Y Liu, BC Bernardo, C Beyer, KI Watt, ... Journal of Cell Biology 203 (2), 345-357, 2013 | 214 | 2013 |
ALS-associated TDP-43 induces endoplasmic reticulum stress, which drives cytoplasmic TDP-43 accumulation and stress granule formation AK Walker, KY Soo, V Sundaramoorthy, S Parakh, Y Ma, MA Farg, ... PloS one 8 (11), e81170, 2013 | 188 | 2013 |
Oral treatment with CuII (atsm) increases mutant SOD1 in vivo but protects motor neurons and improves the phenotype of a transgenic mouse model of amyotrophic lateral sclerosis BR Roberts, NKH Lim, EJ McAllum, PS Donnelly, DJ Hare, PA Doble, ... Journal of Neuroscience 34 (23), 8021-8031, 2014 | 173 | 2014 |
The Hippo pathway effector YAP is a critical regulator of skeletal muscle fibre size KI Watt, BJ Turner, A Hagg, X Zhang, JR Davey, H Qian, C Beyer, ... Nature communications 6 (1), 6048, 2015 | 164 | 2015 |
Diacetylbis (N (4)-methylthiosemicarbazonato) copper (II)(CuII (atsm)) protects against peroxynitrite-induced nitrosative damage and prolongs survival in amyotrophic lateral … CPW Soon, PS Donnelly, BJ Turner, LW Hung, PJ Crouch, NA Sherratt, ... Journal of Biological Chemistry 286 (51), 44035-44044, 2011 | 143 | 2011 |
Association of regulatory T-cell expansion with progression of amyotrophic lateral sclerosis: a study of humans and a transgenic mouse model RK Sheean, FC McKay, E Cretney, CR Bye, ND Perera, D Tomas, ... JAMA neurology 75 (6), 681-689, 2018 | 141 | 2018 |
Antisense peptide nucleic acid‐mediated knockdown of the p75 neurotrophin receptor delays motor neuron disease in mutant SOD1 transgenic mice BJ Turner, IK Cheah, KJ Macfarlane, EC Lopes, S Petratos, SJ Langford, ... Journal of neurochemistry 87 (3), 752-763, 2003 | 128 | 2003 |
Disease mechanisms in ALS: misfolded SOD1 transferred through exosome-dependent and exosome-independent pathways JM Silverman, SM Fernando, LI Grad, AF Hill, BJ Turner, JJ Yerbury, ... Cellular and molecular neurobiology 36, 377-381, 2016 | 112 | 2016 |
SYT1-associated neurodevelopmental disorder: a case series K Baker, SL Gordon, H Melland, F Bumbak, DJ Scott, TJ Jiang, D Owen, ... Brain 141 (9), 2576-2591, 2018 | 104 | 2018 |
Mutant SOD 1 inhibits ER‐Golgi transport in amyotrophic lateral sclerosis JD Atkin, MA Farg, KY Soo, AK Walker, M Halloran, BJ Turner, P Nagley, ... Journal of neurochemistry 129 (1), 190-204, 2014 | 90 | 2014 |
Dysregulation of the complement cascade in the hSOD1G93Atransgenic mouse model of amyotrophic lateral sclerosis JD Lee, NA Kamaruzaman, JNT Fung, SM Taylor, BJ Turner, JD Atkin, ... Journal of neuroinflammation 10, 1-15, 2013 | 86 | 2013 |
Survival motor neuron deficiency enhances progression in an amyotrophic lateral sclerosis mouse model BJ Turner, NJ Parkinson, KE Davies, K Talbot Neurobiology of disease 34 (3), 511-517, 2009 | 86 | 2009 |
SOD1 protein aggregates stimulate macropinocytosis in neurons to facilitate their propagation R Zeineddine, JF Pundavela, L Corcoran, EM Stewart, D Do-Ha, M Bax, ... Molecular neurodegeneration 10, 1-18, 2015 | 85 | 2015 |