Huntingtin suppression restores cognitive function in a mouse model of Huntington’s disease AL Southwell, HB Kordasiewicz, D Langbehn, NH Skotte, MP Parsons, ... Science translational medicine 10 (461), eaar3959, 2018 | 109 | 2018 |
An enhanced Q175 knock-in mouse model of Huntington disease with higher mutant huntingtin levels and accelerated disease phenotypes AL Southwell, A Smith-Dijak, C Kay, M Sepers, EB Villanueva, ... Human molecular genetics 25 (17), 3654-3675, 2016 | 105 | 2016 |
Potent and sustained huntingtin lowering via AAV5 encoding miRNA preserves striatal volume and cognitive function in a humanized mouse model of Huntington disease NS Caron, AL Southwell, CC Brouwers, LD Cengio, Y Xie, HF Black, ... Nucleic acids research 48 (1), 36-54, 2020 | 62 | 2020 |
A novel humanized mouse model of Huntington disease for preclinical development of therapeutics targeting mutant huntingtin alleles AL Southwell, NH Skotte, EB Villanueva, ME Østergaard, X Gu, ... Human Molecular Genetics 26 (6), 1115-1132, 2017 | 37 | 2017 |
Altering cortical input unmasks synaptic phenotypes in the YAC128 cortico-striatal co-culture model of Huntington disease ME Schmidt, C Buren, JP Mackay, D Cheung, L Dal Cengio, LA Raymond, ... BMC biology 16, 1-12, 2018 | 20 | 2018 |
DAPK1 promotes extrasynaptic GluN2B phosphorylation and striatal spine instability in the YAC128 mouse model of Huntington disease ME Schmidt, NS Caron, AE Aly, FL Lemarié, L Dal Cengio, Y Ko, N Lazic, ... Frontiers in Cellular Neuroscience 14, 590569, 2020 | 14 | 2020 |
BMAL1 loss in oligodendroglia contributes to abnormal myelination and sleep D Rojo, L Dal Cengio, A Badner, S Kim, N Sakai, J Greene, T Dierckx, ... Neuron 111 (22), 3604-3618. e11, 2023 | 3 | 2023 |
BMAL1 loss in oligodendroglial lineage cells dysregulates myelination and sleep D Rojo, A Badner, L Dal Cengio, S Kim, N Sakai, J Greene, E Eisinger, ... bioRxiv, 2022.04. 28.489946, 2022 | 1 | 2022 |
I09 Antibodies inhibit cell to cell transmission of mutant HTT S Bartl, A Oueslati, AL Southwell, M Parth, N Salhat, A Siddu, M Burkert, ... Journal of Neurology, Neurosurgery & Psychiatry 89 (Suppl 1), A91-A91, 2018 | 1 | 2018 |
Corrigendum to" Reducing huntingtin by immunotherapy delays disease progression in a mouse model of Huntington disease"[Neurobiology of Disease, 2024 Jan: 190: 106376] S Bartl, Y Xie, N Potluri, R Kesineni, K Hencak, L Dal Cengio, K Balazs, ... Neurobiology of disease, 106444, 2024 | | 2024 |
Reducing huntingtin by immunotherapy delays disease progression in a mouse model of Huntington disease S Bartl, Y Xie, N Potluri, R Kesineni, K Hencak, L Dal Cengio, K Balazs, ... Neurobiology of Disease 190, 106376, 2024 | | 2024 |
What do Nursing Students’ Stories Reveal about the Development of their Technological Skills and Digital Identity? A Narrative Inquiry L Dal Cengio, et. al. (in collaboration BSN-AE) Canadian Journal of Nursing Informatics 15 (1), 2020 | | 2020 |