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| Distinct brain transcriptome profiles in C9orf72-associated and sporadic ALS M Prudencio, VV Belzil, R Batra, CA Ross, TF Gendron, LJ Pregent, ... Nature neuroscience 18 (8), 1175-1182, 2015 | 423 | 2015 |
| Aggregation-prone c9FTD/ALS poly (GA) RAN-translated proteins cause neurotoxicity by inducing ER stress YJ Zhang, K Jansen-West, YF Xu, TF Gendron, KF Bieniek, WL Lin, ... Acta neuropathologica 128, 505-524, 2014 | 423 | 2014 |
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| Poly(GR) impairs protein translation and stress granule dynamics in C9orf72-associated frontotemporal dementia and amyotrophic lateral sclerosis YJ Zhang, TF Gendron, MTW Ebbert, AD O’Raw, M Yue, K Jansen-West, ... Nature medicine 24 (8), 1136-1142, 2018 | 314 | 2018 |
| Variation in aggregation propensities among ALS-associated variants of SOD1: correlation to human disease M Prudencio, PJ Hart, DR Borchelt, PM Andersen Human molecular genetics 18 (17), 3217-3226, 2009 | 304 | 2009 |
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| Spt4 selectively regulates the expression of C9orf72 sense and antisense mutant transcripts NJ Kramer, Y Carlomagno, YJ Zhang, S Almeida, CN Cook, TF Gendron, ... Science 353 (6300), 708-712, 2016 | 140 | 2016 |
| Long-read sequencing across the C9orf72 ‘GGGGCC’ repeat expansion: implications for clinical use and genetic discovery efforts in human disease MTW Ebbert, SL Farrugia, JP Sens, K Jansen-West, TF Gendron, ... Molecular neurodegeneration 13, 1-17, 2018 | 127 | 2018 |
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Dennis W. DicksonMayo ClinicVerified email at mayo.edu
